Anaesthesia for diagnostic muscle biopsy in an infant with Pompe's disease.
نویسندگان
چکیده
The anaesthetic management of children with glycogen-storage disease type IIa (Pompe's disease) presents a variety of challenges. A modification of a femoral nerve block, the inguinal paravascular block, as described by Winnie, was used in conjunction with intravenous ketamine to provide anaesthesia for a diagnostic muscle biopsy in a 5.5-month-old infant with Pompe's disease. A peripheral nerve stimulator was used to locate the femoral nerve in lieu of eliciting a paraesthesia.
منابع مشابه
Ketamine monoanaesthesia for diagnostic muscle biopsy in neuromuscular disorders in infancy and childhood: floppy infant syndrome.
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ورودعنوان ژورنال:
- Canadian Anaesthetists' Society journal
دوره 33 6 شماره
صفحات -
تاریخ انتشار 1986